Coronary Sinus Atrial Septal Defect (Unroofed Coronary Sinus) with Total Anomalous Pulmonary Venous Connection—A Case Report
نویسندگان
چکیده
Introduction: To present a rare occurrence of coronary sinus atrial septal defect (ASD) associated with total anomalous pulmonary venous connection (TAPVC). Case Report: A 16-year-old girl was diagnosed with features of an atrial septal defect (ASD) by transthoracic echocardiography and the absence of PLSVC (persistent left superior vena cava) connection to coronary sinus was confirmed by saline contrast echocardiography (“bubble study”). Discussion: The cause of the dilated coronary sinus was due to total anomalous pulmonary venous connection. Conclusion: Coronary sinus atrial septal defect (ASD) is a rare interatrial shunt that is commonly associated with a persistent left superior vena cava (PLSVC) and occurs in less than 1% of cases of ASDs. It is characterized by the absence of at least a portion of the common wall that separates the coronary sinus and left atrium. Isolated defects are associated with low rate of morbidity and mortality.
منابع مشابه
Surgery for total anomalous pulmonary venous connection and long term follow up
Methods In the period between January 1998 and April 2013, 84 patients (48 boys) underwent repair for total anomalous pulmonary venous connection. Their ages ranged from 2 weeks to 1.6 years (mean 4 months). The patients’ weight ranged from 3 to 8 kg (mean 5 kg). About 71% of patients (n = 60) were less than the 50th percentile of predicted weight for age and sex. The anomalous connection was s...
متن کاملUnroofed coronary sinus defect.
Subsequent echocardiogram showed a dilated right ventricle with moderate tricuspid regurgitation. There was pulmonary hypertension (estimated pulmonary arterial systolic pressure, 55 mm Hg). Transthoracic Doppler studies showed a left-to-right shunt with a shunt ratio of 2:1. However, the ductus arteriosus was not patent and there were no septal defects. The coronary sinus was dilated and there...
متن کاملAtrial Septal Defects in the Adult
Nomenclature and Classification There are 3 major types of ASDs or interatrial communications: ostium secundum, ostium primum, and sinus venosus (Figure 1A) defects. The ostium secundum is a true defect of the atrial septum and involves the region of the fossa ovalis. The ostium primum defect is within the spectrum of the atrioventricular (AV) septal defects (Figure 1B; also known as AV canal d...
متن کاملSuccessful total correction of complete atrioventricular canal, total anomalous pulmonary venous drainage and unroofed coronary sinus in an infant.
An infant with complete atrioventricular canal, total anomalous pulmonary venous drainage into the left superior vena cava and an unroofed coronary sinus successfully underwent total correction. A homograft vein was used to connect the proximal left superior vena cava to the right atrium and can be recommended when other methods of correction of unroofed coronary sinus cannot be used.
متن کاملBiventricular repair of complete atrioventricular canal, double-outlet right ventricle and common atrium using a modified double switch technique. A valid alternative to univentricular procedure.
An eleven month-old child underwent a successful modified double switch operation for total correction of complete atrioventricular canal, double outlet right ventricle, noncommitted ventricular septal defect, pulmonary stenosis, common atrium and anomalous left superior vena cava to an unroofed coronary sinus. We describe the technique of modified double switch operation, utilizing an atrial s...
متن کامل